Monomelic Amyotrophy

Monomelic amyotrophy is a rare benign lower motor neuron disorder predominantly affecting young males, characterized by unilateral distal upper limb weakness and atrophy. Etiology is unclear, though it may involve cervical spinal cord ischemia or mechanical compression. Pathophysiology involves selective anterior horn cell degeneration. Diagnosis relies on clinical examination and electrophysiology. Management is supportive, including physiotherapy; prognosis is generally favorable with slow progression or stabilization.